Describe the use and benefits of sapropterin dihydrochloride.

What will be an ideal response?


Sapropterin dihydrochloride is an oral formulation of the biologically active tetrahydrobiopterin, cofactor to the phenylalanine hydroxylase enzyme. Sapropterin is effective in lowering blood Phe levels in some individuals with PKU by activating residual activity of the PAH enzyme. Sapropterin improves dietary Phe tolerance, allowing more dietary consumption of natural sources of protein.

Nutritional Science

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A husband and wife who both have type 2 diabetes are taking part in a weight loss program. The woman asks why her husband, who has the same starting height and weight, has lost more weight than her despite identical interventions. What is the nurse's best response?

Nutritional Science

Most commonly, kidney function is measured by the _______________.

Fill in the blank(s) with the appropriate word(s).

Nutritional Science

A tumor that infiltrates the bone marrow results in what type of cancer?

a. Leukemia b. Carcinoma c. Sarcoma d. Lymphoma

Nutritional Science

A fatty acid that has a single double bond is called a

A) unsaturated fatty acid. B) polyunsaturated fatty acid. C) saturated fatty acid. D) monounsaturated fatty acid.

Nutritional Science