Describe supplementation of end products as an approach for chronic management of metabolic disorders and provide a specific example
Substrates that should have been formed from the enzymatic reactions that are defective in metabolic disorders are needed for energy production, protein turnover, feedback inhibition of metabolic pathways, and/or production of other substrates. In the case of metabolic blocks in these enzymatic reactions, an alternative means of achieving the end goal of the reaction must be provided. In glycogen storage disease type I, for example, the enzymatic block results in an inability to produce glucose. Consequently, providing a continuous source of glucose through frequent feedings is the therapy for this disorder. Similarly, in the amino acid disorder homocystinuria, where the amino acid homocysteine is unable to be converted to cysteine, cysteine consequently needs to be supplemented in the diet.
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_______________ starch is defined as starch components that enter the large intestine undigested
Fill in the blank(s) with correct word
Sweetened dressings are usually reserved for
A. green salads. B. vegetable salads. C. fruit salads. D. protein-based salads.
Fiber is not an especially important nutrient in a young child's diet
Indicate whether the statement is true or false
Most seltzers become bubbly by the commercial addition of pressurized _____
a. carbon dioxide b. nitrogen c. hydrogen d. oxygen e. sodium chloride