Describe the use and benefits of sapropterin dihydrochloride


Sapropterin dihydrochloride is an oral formulation of the biologically active tetrahydrobiopterin, cofactor to the phenylalanine hydroxylase enzyme. Sapropterin is effective for lowering blood Phe levels in some individuals with PKU by activating residual activity of the PAH enzyme. Sapropterin improves dietary Phe tolerance, allowing more dietary consumption of natural sources of protein.

Nutritional Science

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The functional assessment component for a nutritional status assessment of older adults measures _____

a. liver function b. cardiac output c. activities of daily living d. risk of malnutrition

Nutritional Science

Which of the following groups of people is most likely to be successful in making positive dietary changes?

a. "Vacillating" consumers b. "Unconcerned" consumers c. "Pre-contemplation" consumers d. "Committed" consumers

Nutritional Science

For a patient suffering from a disease, but who is obtaining enough kcal each day, protein requirements should be met by providing ____ g/kg/day

a. 0.8 b. 1.5 c. 1.8 d. 2.0 e. 2.4

Nutritional Science

In order to reach students and catalyze change, education should be ____

a. amusing, aggregated, and fact-based b. challenging, variegated, and results-oriented c. fun, integrated, and behaviorally based d. difficult, delegated, and detail-oriented

Nutritional Science