Describe the effects that the two rare genetic disorders, Menkes disease and Wilson’s disease, have on copper status and the treatment for both

What will be an ideal response?


These two disorders affect copper status in opposite directions. In Menkes disease, the intestinal cells absorb copper but cannot release it into circulation, causing a life-threatening deficiency. Treatment involves giving copper intravenously. In Wilson’s disease, copper accumulates in the liver and brain, creating a life-threatening toxicity. Wilson’s disease can be controlled by reducing copper intake, using chelating agents such as penicillamine, and taking zinc supplements, which interfere with copper absorption.

Nutritional Science

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Which of the following describes a connection between physical activity and energy expenditure?

a. The number of kcalories spent in an activity depends on body weight, intensity, and duration. b. Walking a mile uses about half as much energy as running a mile c. Exercising the leg muscles is effective at burning away fat primarily around the thighs and hips d. Exercising the abdominal muscles is effective at burning away fat primarily around the abdomen e. If intensity and duration are the same, heavier individuals will expend less energy running than will lighter individuals.

Nutritional Science

According to the Physical Activity Guidelines for Americans, how much time, at a minimum, should children spend being physically active per week?

a. 30 minutes a day, at least 5 days a week b. 45 minutes a day, at least 5 days a week c. 60 minutes a day, preferably 7 days a week d. 90 minutes a day, preferably 7 days a week

Nutritional Science

A subcategory of anorexia nervosa characterized by food avoidance or excessive exercise is called the

A. restricting type. B. binge eating type. C. purging type. D. None of the above

Nutritional Science

Symptoms of salmonellosis typically begin from ____________ hours after eating. ?

A) ?1-2 B) 12-72 C) ?6-48 D) 12-36

Nutritional Science