A pediatric nurse is reviewing the chart of a new school-age patient. The chart notes the child is on a phenylalanine-free diet. What does the nurse conclude about this patient?

A.
Has Canavan disease
B.
Has familial dysautonomia
C.
Has phenylketonuria (PKU)
D.
Has Tay-Sachs disease


ANS: C
Children with PKU are born without an enzyme to metabolize the amino acid phenylalanine. If not treated with a life-long phenylalanine-free diet, the child can have severe mental and physical retardation. The other diseases do not require this diet.

Nursing

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A physician is providing care for a child who has a diagnosis of cystic fibrosis (CF). Place the following events in the etiology of CF in ascending chronological order. Use all the options

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A client is recovering from a hysteroscopic myomectomy. The nurse assesses the client and finds the following: 2+ bilateral pedal edema; pulse, 108 beats/min; and respiratory rate, 28 breaths/min. Which action by the nurse takes priority?

a. Assess lung sounds and oxygen saturation. b. Call for an immediate electrocardiogram (ECG). c. Notify the health care provider as soon as possible. d. Review the client's intake and output pat-tern.

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A client is being discharge after successful CABG surgery. Despite the positive prognosis, the nurse cautions the client and family that

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The labor and delivery unit nurse manager is incorporating complementary and alternative therapies into the unit's policies and procedures

Which statement should the nurse manager make to the nursing staff during an in-service educational presentation? 1. "Policies have been developed for using massage and aromatherapy." 2. "When patients ask questions you don't know, tell them to look online." 3. "Because herbs are dangerous during pregnancy, we will not use them." 4. "Be sure to ask patients what alternative therapies they have used."

Nursing