Describe the difference between congenital malformations and inborn errors of metabolism. Cite one example of an inborn error of metabolism and describe the best nutrition-related intervention


Congenital malformations are structural abnormalities in the fetus while inborn errors of metabolism are metabolic abnormalities in the fetus. Phenylketonuria is an inherited error in phenylalanine metabolism most commonly caused by a deficiency of phenylalanine hydroxylase, which converts the essential amino acid phenylalanine to the nonessential amino acid tyrosine. Phenylketonuria can be successfully managed by a low-phenylalanine diet. High phenylalanine protein foods such as meat, fish, eggs, and wheat are excluded from the diet. Supplemental DHA (200 mg per day) should be consumed because PKU diets lack dietary sources of this important omega-3 fatty acid.

Nutritional Science

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The disaccharides important in nutrition are sucrose, maltose, and

A. fructose. B. galactose. C. dextrose. D. lactose.

Nutritional Science

Which group is at greatest risk of contracting a foodborne illness?

A. a 35-year-old basketball coach, a 70-year-old grandmother, and a 45-year-old professor B. a 70-year-old grandmother, a 2-year-old, and a teenage boy C. a 45-year-old professor, a middle-age woman who has diabetes, and a teenage boy D. a 70-year-old grandmother, a 2-year-old, and a middle-age woman who has diabetes

Nutritional Science

Sodium and potassium ions are electrolytes.

Answer the following statement true (T) or false (F)

Nutritional Science

The mother stores protein in the maternal anabolic phase of pregnancy

Indicate whether the statement is true or false

Nutritional Science